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Two center experience in multidisciplinary treatment of Dandy-Walker syndrome / G. Posiunas, E. Lukosevicius, A. Drukteiniene, V. Daugelavicius, V. Barauskas
Type of publication
Tezės kitame recenzuojamame leidinyje / Theses in other peer-reviewed publication (T1e)
Author(s)
Pošiūnas, Gintautas | |
Drukteinienė, Asta | Šiaulių universitetas |
Daugelavičius, Vidūnas | |
Title
Two center experience in multidisciplinary treatment of Dandy-Walker syndrome / G. Posiunas, E. Lukosevicius, A. Drukteiniene, V. Daugelavicius, V. Barauskas
Publisher (trusted)
Rīga Stradiņŝ university |
Date Issued
Date Issued |
---|
2012-05-17 |
Extent
p. 50, no. O. 29.
Is part of
The 12th Conference of the Baltic Association of Paediatric Surgeons : May 17-19, 2012, Riga, Latvia : Fianal programme and abstracts / University Children's Hospital of Latvia, Rīga Stradiņŝ university ; Editor: Maija Treilona. Riga : Rīga Stradiņŝ university, 2012. ISBN 978-9984-793-03-0.
Version
Originalus / Original
Series/Report no.
Varies.
Field of Science
Keywords
Abstract
Introduction.Dandy-Walker syndrome is a rare congenital malformation that involves multiple systems and organs. This malformation is characterized by agenesis or hypoplasia of cerebellar vermis, cystic dilatation of the fourth ventricle, and enlargement of the posterior fossa also could have associated multiple abnormalities. Objective. To present the multidisciplinary treatment results of Dandy-Walker syndrome. Materials and methods. Imaging, case histories, surgical protocols were analyzed of the patient with Dandy–Walker syndrome. Results Diagnosis of Dandy-Walker malformation was made postnatally after detailed examination in Kaunas. Patient had hydrocephalus, hypoplasia of cerebellar vermis, cystic dilatation of the fourth ventricle, enlargement of the posterior fossa, sternal cleft, tracheomalacia, large bilateral hemangiomas of face and neck, microstomia. At the age of 3 weeks patient was operated on due to sternal cleft, thoracoplasty was performed. Later patient was operated on by neurosurgeons, shunting of fourth ventricle was done. After these corrections in Kaunas, for the next treatment patient was transferred to Children’s Hospital in Vilnius. Steroid therapy was administered for 6 months due to rapidly growing facial hemangiomas. Later multiple laser treatments of hemangiomas by Nd:YAG and pulsed dye laser were performed. Because of microstomia and feeding problems craniofacial surgeon did oral plastic surgery. Now patent is socially active, neurologically compensated and have satisfactory cosmetic appearance. Conclusion Despite pure prognosis of Dandy-Walker syndrome, multidisciplinary treatment and teamwork could achieve good results in the treatment of this rare disease.
Type of document
type::text::conference output::conference proceedings::conference paper
ISBN (of the container)
978-9984-793-03-0
Other Identifier(s)
(LSMU ALMA)990000795560107106
Coverage Spatial
Latvija / Latvia (LV)
Language
Anglų / English (en)